Functional muscle impairment in facioscapulohumeral muscular dystrophy is correlated with oxidative stress and mitochondrial dysfunction
Keywords
ROS
double homebox 4 gene
GSSG
T Lim
MVC
Lipofuscin
Facioscapulohumeral muscular dystrophy (FSHD) 4-Hydroxy-2-nonenal Thiobarbituric acid-reactive substances Lipofuscin Oxidative stress Protein oxidation Radical oxygen species Mitochondria dysfunction Antioxidants Abbreviations: FSHD
Cu-SOD
Facioscapulohumeral muscular dystrophy (FSHD)
U1046
HNE
TBARS
oxidized glutathione
reactive oxygen species
manganese-dependent superoxide dismutase
DUX4
Bâtiment Crastes de Paulet
Oxidative stress
endurance limit time
maximal voluntary contraction
thiobarbituric acid-reactive substances
4-hydroxy-2-nonenal
2-MWT
MnSOD
facioscapulohumeral dystrophy
reduced glutathione
GSH
copper-zinc-dependent superoxide dismutase
glutathione reductase
Protein oxidation
GR
Mitochondria dysfunction
Radical oxygen species
2 minute walking test n Correspondence to: INSERM
Antioxidants
Domains
Life Sciences [q-bio]
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